[1]王佚,孙静.苗勒管发育不全综合征合并先天性肛门直肠畸形的临床研究新焦点[J].第三军医大学学报,2018,40(23):2126-2130.
 WANG Yi,SUN Jing.New focuses in diagnosis and treatment of Mayer-Rokitanski-Küster-Hauser syndrome with congenital anorectal malformation[J].J Third Mil Med Univ,2018,40(23):2126-2130.
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苗勒管发育不全综合征合并先天性肛门直肠畸形的临床研究新焦点(/HTML )
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《第三军医大学学报》[ISSN:1000-5404/CN:51-1095/R]

卷:
40卷
期数:
2018年第23期
页码:
2126-2130
栏目:
专题报道
出版日期:
2018-12-15

文章信息/Info

Title:
New focuses in diagnosis and treatment of Mayer-Rokitanski-Küster-Hauser syndrome with congenital anorectal malformation
作者:
王佚孙静
重庆医科大学附属儿童医院胃肠新生儿外科
Author(s):
WANG Yi SUN Jing

Department of Gastrointestinal Neonatal Surgery, Children’s Hospital of Chongqing Medical University, Chongqing, 400014, China

关键词:
苗勒管发育不全综合征先天性肛门直肠畸形治疗
Keywords:
Mayer-Rokitanski-Küster-Hauser syndrome anorectal malformation surgical treatment
分类号:
R726.571; R726.911
文献标志码:
A
Abstract:

Mayer-Rokitanski-Küster-Hauser (MRKH)  syndrome with congenital anorectal malformations (ARM) is a rare disease in children, which involves the female anorectal and reproductive system. Treatment and prognosis for this condition are still inconclusive. Although the understanding for congenital ARM has been deepened in recent years, attentions having been paid to MRKH syndrome with ARM are far from enough. Its treatment and timing are controversial. Rectal vestibular fistula is the most common type of female imperforate anus. When the exact vaginal opening has not been identified by perineal examination, the complication of MRKH syndrome should be considered. This article systematically reviewed the clinical diagnosis, treatment, timing and prognosis of MRKH syndrome with imperforate anus.

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相似文献/References:

[1]孙静,王至立,侯金凤,等.横结肠袢式造口术在先天性肛门直肠畸形分期手术中应用的临床研究[J].第三军医大学学报,2017,39(18):1848.
 SUN Jing,WANG Zhili,HOU Jinfeng,et al.Transverse-loop colostomy in phased treatment of congenital anorectal malformation[J].J Third Mil Med Univ,2017,39(23):1848.
[2]韩一江,黄寿奖,秦琪,等.先天性球形结肠的临床特点和诊治体会[J].第三军医大学学报,2018,40(23):2131.
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更新日期/Last Update: 2018-12-18